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Conditions treated by the Single Ventricle Service

The Single Ventricle Service looks after children with the following conditions:

Double Inlet Ventricle

Double Inlet Ventricle is a condition where both upper filling chambers (atria) pump blood into one of the pumping chambers (ventricle), resulting in one larger ventricle and one small ventricle.

Ebstein Anomaly

Ebstein's anomaly is a condition in which the valve on the right side of the heart (the tricuspid valve), which separates the right atrium and right ventricle, doesn't develop properly.

This means blood can flow the wrong way within the heart, and the right ventricle may be smaller and less effective than normal.

Hypoplastic Left Heart Syndrome

Hypoplastic left heart syndrome is a condition where the left lower pumping chamber (left ventricle) of the heart does not develop properly so is much smaller than usual. The mitral valve between the left ventricle and the upper left filling chamber (left atrium) is often closed or very small

Pulmonary Atresia with Intact Ventricular Septum

Pulmonary atresia with intact ventricular septum is comprised of two main abnormalities. The pulmonary valve, which allows blood to flow from the heart into the lungs, is completely blocked. Additionally, the right ventricle, which pumps blood to the lungs, has not developed as normal. This means that oxygen cannot be delivered to the body the way it should.

Shone's Complex

Shone's complex is a congenital heart defect that affects how blood flows into and out of the left side of the heart. It consists of multiple abnormalities that result in blood being unable to flow through the left side, causing symptoms of congestive heart failure.

Tricuspid Atresia

Tricuspid atresia is a condition in which the valve linking the right ventricle and the right atrium (tricuspid valve) is closed or missing, resulting in a small right ventricle.

Unbalanced atrioventricular septal defect (AVSD)

An atrioventricular septal defect results in a is a large hole between the upper filling chambers (atria) and the lower pumping chambers (ventricles) of the heart. There is also only one valve between the atria and ventricles instead of two. In some children, either the right or the left side of the heart may be underdeveloped. This is known as an unbalanced AVSD.

Conditions with two ventricles

The Single Ventricle Service also looks after children with two adequate ventricles, which cannot be separated surgically. This includes the following conditions:

Atrioventricular septal defect with AV valve straddle
Criss-cross heart
Complex heterotaxy

Further information

For more information about these conditions, please see the fact sheet on the British Heart Foundation's website.

Please note, this list is not exhaustive and the team looks after children with other specialised conditions which may not be listed on this page.